Pulmonary artery aneurysm is Behcet's disease is rare and can be fatal due to rupture.
We experienced a case of pulmonary artery aneurysm in Behcet's disease. The patient was 21 year old woman who was admitted with three month history of dyspnea, fever and cough. On examination, she had aphthous ulcer in the mouth and erythema
nodosum on
the left popletial fossa and forearm, but didn't have any lesion at eyes and genitalia.
The latex fixation test for rheumatoid factor, VDRL test for syphillis, antinuclear antibody and LE cell test were all negatives. The third and fourth components of complement in the serum, serum immunoglobulin concentrations(IgG, IgM, IgA) were
within
normal range.
The chest radiography revealed a 6×7cm. The IV-DSA showed a single aneurysm at the proximal part of left 140wer lobe artery with lingular segment artery and no distal perfusion by thombotic obstruction.
The steroid therapy was done for a month, but symptoms not improved. We performed resection of lingular segment and lower lobe including the aneurysm.
The microscopic findings of the operative specimen were intimal hyperplasia and fragmentation of the internal elastic fibers.
She Was improved without remarkable event, except infection of the operative wound.
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